Mapleflex (MSUD ages 1-10 years)
Nutritional value per serving
Serving Information
Amount per 100 grams / 100 ml of product
| Nutrition Information | per 100g powder | per 29g sachet |
| Energy kJ | 1639 | 474 |
| kcal | 390 | 113 |
| Protein Equivalent g | 29 | 8.4 |
| Total Amino Acids g | 35 | 10 |
| Carbohydrate g | 38 | 11 |
| of which sugars | 3.8 | 1.1 |
Description
Mapleflex is an unflavoured leucine, isoleucine and valine free powdered drink mix containing essential and non-essential amino acids, fat, carbohydrate, vitamins, minerals and trace elements. A food for special medical purposes.http://nutrition.nutricia.com/images/uploads/Mapleflex.jpg
Indications and Prescribability
Mapleflex is for the dietary management of Maple Syrup Urine Disease in children aged 1-10 years. It contains a balanced blend of essential fatty acids (4:1) as children with MSUD have been shown to have higher levels of linoleic acid, and lower levels of linolenic acid compared to controls and low plasma DHA levels. Initial case studies indicate that Mapleflex is well tolerated and growth and biochemical indices are normal.
Suggested Intake
The quantity of Mapleflex should be determined by a clinician or a dietitian only and is dependent on the age, bodyweight, and medical condition of the patient.
The diet must be supplemented with some natural protein and other nutrients in medically prescribed quantities to meet the leucine, isoleucine, valine and general nutrient requirements of the patient.
Preparation & Administration
Mapleflex is best presented as a chilled drink but can also be given as a paste.
As a drink:
The recommended dilution is 1 sachet of Mapleflex (29g) plus 100ml of water.
As a paste:
Mix one sachet of Mapleflex with 30ml of water. If taken as a paste additional water or diluted drinks must be consumed at the same time.
The osmolality of Mapleflex at the above dilution is 1130 mosm/kg.
Precautions
Use under medical supervision.
Not suitable for use as a sole source of nutrition
Not for parenteral use.
Not suitable for infants.
Precautions
Store in a cool, dry place.
Pack Size
30 x 29g sachets
Notes
Shelf life: 1 year.